Fatty Acid Oxidation Disorders
Principles of the disturbances of energy production from long-chain fatty acids
The term "metabolism" encompasses all processes necessary for building the body, maintaining bodily functions, and obtaining energy. To fulfill these tasks, the food ingested or reserves stored in the body are processed in many carefully coordinated steps. These steps are facilitated by enzymes and transporters. Each step in metabolism requires its own enzyme. If a specific enzyme in the body doesn't function properly, it can lead to a metabolic disorder where the corresponding metabolic step cannot proceed correctly. Due to the numerous different metabolic steps, there are also many different metabolic disorders. The metabolism of fatty acids serves to provide energy for the body and its organs.